What is Rasmussen's Encephalitis?
Rasmussen's Encephalitis is a rare brain disease. It was originally diagnosed in 1958,
by Dr. Rasmussen’s of Montreal Canada. The disease is an extremely rare neurological disorder
that causes severe uncontrollable seizures. The disease affects children ususally under the
age of 10, both boys and girls. Most people with this disease will experience frequent
seizures and brain damage over the course of the first 8 to 12 months, and then enter
a phase of permanent neurological deficits.
What are the Signs and Symptoms
- Rasmussen's Encephalitis often has a quick onset wherein the child begins
having petite mal seizures that start as staring episodes which then graduate into partial
complex seizures and then full blown tonic clonic type seizures, in other words Grand malls. A
Grand mal is where the child shakes violently.
- Uncontrollable seizures can damage a young child’s brain. It can deplete the brain of
oxygen and cause serious brain damage.
- Another characterization is shown by continued frequent and severe seizures that are
resistant to treatment, encephalitis (which is inflammation of the brain), hemi paresis
(paralysis on one side of the body), dementia (the loss of intellect and emotional disturbances), the
loss of motor skills and speech, and even metal deterioration.
What are the Causes?
- No one really knows for sure.
- Scientists and doctors suspect either a viral infection that enters the body and settles
in the brain and/or some type of an auto-immune disease.
What is the Diagnosis and Treatment?
Besides the obvious signs and symptoms, doctor use other methods to help diagnosis Rasmussens
Encephalitis.
- These include tests such as EEG monitoring (an electroencephalogram test that measures and records
the electrical activity of your brain), CAT scans (X-rays), MRI’s (magnetic resonance imaging
test that uses a magnetic field and pulses of radio wave energy to make pictures of organs and
structures), and PET scan (Positron emission tomography test that combines computed tomography and
nuclear scanning scans).
- The most frequent and usually most beneficial method of treatment is a hemispherectomy,
removal of half the brain. This is what Brandi underwent, removing the entire right hemisphere.
What is a Hemispherectomy?
A Hemispherectomy is a surgical procedure where one cerebral hemisphere (half of the brain)
is removed or disabled. This disconnections the communication between the two hemispheres,
which prevents the spread of seizures to the functional side of the brain. A hemispherectomy is only
for people who dont experience any improvement in their condition after having taken medication or for
those who have very severe uncontrollable seizures in one half of their brain.
- According to WebMDHealth, about 85% of people who have a functional hemi will experience
significant improvement.
- About 60% will become seizure-free.
- In many cases, most frequently in children, the remaining half of the brain takes over
the tasks that used to be controlled by the section that was infected.
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